{"id":9158,"date":"2021-12-12T20:28:25","date_gmt":"2021-12-12T18:28:25","guid":{"rendered":"https:\/\/meddists.com\/learn\/pre-clinical\/biochemistry\/biochemistry-of-the-metabolism\/amino-acid-metabolism\/smelly-diseases\/"},"modified":"2021-12-12T20:39:07","modified_gmt":"2021-12-12T18:39:07","slug":"smelly-diseases","status":"publish","type":"page","link":"https:\/\/meddists.com\/learn\/pre-clinical\/biochemistry\/biochemistry-of-the-metabolism\/amino-acid-metabolism\/smelly-diseases\/","title":{"rendered":"Smelly diseases"},"content":{"rendered":"\n

Diseases related to amino acid metabolism can be categorized not only by the enzyme reaction but also the smell is indicative in these cases<\/div><\/p>\n\n\n\n
Disorder<\/strong><\/td>Urine odour<\/strong><\/td><\/tr>
Phenylketonuria (PKU)<\/td>“musty” or “mousy” <\/td><\/tr>
Cystinuria<\/td>“sulphur” <\/td><\/tr>
Isovaleric acidemia<\/td>“sweaty feet” <\/td><\/tr>
3-Methylcrotonylglycinuria<\/td>\u201emale cat urine\u201d<\/td><\/tr>
Methionine malabsorption<\/td>“cabbage”<\/td><\/tr>
Tyrosinemia<\/td>“cabbage” or “rancid butter”<\/td><\/tr>
Methylmalonic academia<\/td>“acidic”<\/td><\/tr>
Maple syrup urine disease (MSUD)<\/td>“curry” or “maple syrup” or “burnt sugar”<\/td><\/tr><\/tbody><\/table><\/figure>\n\n\n\n

References<\/h2>\n<\/span>\n\n\n

Snider MDS. Devlin\u2019s Textbook of Biochemistry with Clinical Correlations<\/strong>, the 8th Edition. John Wiley & Sons, Incorporated, 2020; 2019.<\/span> <\/p>\n<\/span>

References<\/h2><\/div>","protected":false},"excerpt":{"rendered":"

Disorder Urine odour Phenylketonuria (PKU) “musty” or “mousy” Cystinuria “sulphur” Isovaleric acidemia “sweaty feet” 3-Methylcrotonylglycinuria \u201emale cat urine\u201d Methionine malabsorption “cabbage” Tyrosinemia “cabbage” or “rancid butter” Methylmalonic academia “acidic” Maple syrup urine disease (MSUD) “curry” or “maple syrup” or “burnt sugar” References Snider MDS. Devlin\u2019s Textbook of Biochemistry with Clinical Correlations, the 8th Edition. John […]<\/p>\n","protected":false},"author":23,"featured_media":0,"parent":1714,"menu_order":28,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-9158","page","type-page","status-publish","hentry"],"yoast_head":"\nSmelly diseases – Meddists<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/meddists.com\/learn\/pre-clinical\/biochemistry\/biochemistry-of-the-metabolism\/amino-acid-metabolism\/smelly-diseases\/\" \/>\n<meta name=\"twitter:label1\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" 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